Ornithine translocase is responsible for transporting ornithine from the cytosol into the mitochondria in the urea cycle. It is highly expressed in the liver and pancreas.
solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 15 | |||||||
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Identifiers | |||||||
Symbol | SLC25A15 | ||||||
Alt. symbols | ORNT1, HHH | ||||||
NCBI gene | 10166 | ||||||
HGNC | 10985 | ||||||
OMIM | 603861 | ||||||
RefSeq | NM_014252 | ||||||
UniProt | Q9Y619 | ||||||
Other data | |||||||
Locus | Chr. 13 q14 | ||||||
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A disorder is associated with ornithine translocase deficiency, and a form of hyperammonemia.